前言目的探讨特发性腹膜后纤维化（IRF）的临床特点及诊治原则。方法回顾性分析近8年收治的27例IRF患者临床资料。结果腹痛、腰痛、腹膜后包块及输尿管梗阻为主要临床表现。影像学检查为主要诊断手段。术前诊断正确率为852%。21例合并输尿管梗阻,行输尿管松解、大网膜包裹移位术;2例合并肾动脉狭窄,行肾动脉松解术、IRF包块切除术;1例合并肠系膜上动脉压迫,行松解术;另3例无梗阻,仅做活检。术后1例死亡,26例临床治愈。结论IRF无特异性临床表现,术前诊断主要依据影像学检查。治疗主要解除压迫症状。
ObjectiveToinvestigatetheclinicalcharacteristicsofidiopathicretroperitonealfibrosis（IRF）anditsdiagnosisandtreatment.MethodsDataof27IRFcasesadmittedintoourhospitalduringrecent8yearswereretrospectivelyanalyzed.ResultThemainclinicalmanifestationsofIRFincludedabdominalpain,lumbago,massinretroperitonealcavityandureteralobstruction.ThemaindiagnosticapproachtoIRFwastheimageexamination.Preoperativecorrectdiagnosiswasestablishedin852%ofcases.Ure...
